Clinical features and surgical outcomes of encircling scleral buckling with cryotherapy in familial exudative vitreoretinopathy-associated rhegmatogenous retinal detachment Encircling buckling for FEVR-RRD.

PURPOSE To report the clinical features and surgical outcomes of encircling scleral buckling (ESB) surgery with cryotherapy in familial exudative vitreoretinopathy (FEVR) patients with rhegmatogenous retinal detachment (RRD). METHODS This study was a consecutive, retrospective interventional case series. Clinical features, including the FEVR stage, proliferative vitreoretinopathy (PVR) grade, range of retinal detachment and degeneration, and presence of retinal breaks, and surgical outcomes, including the success rate, best-corrected visual acuity (BCVA) and myopic shift, were analyzed. RESULTS There were 16 eyes with stage 3A FEVR and 8 eyes with stage 4A FEVR. Thirteen eyes had grade A PVR, and 11 eyes had grade B PVR. Retinal reattachment was achieved in 22 of 24 eyes (91.67%) with FEVR-RRD after initial ESB surgery. The BCVA improved from a mean of 1.08±0.86 logarithm of the minimum angle of resolution (logMAR) preoperatively to 0.45±0.41 logMAR postoperatively (P<0.01). A myopic shift of -2.39±1.38 (range, -1 to -6) diopter (P<0.01) was observed. The mean follow-up period was 34.5±27.7 (range, 7-104) months. CONCLUSIONS Our study clarified the efficacy of ESB surgery with cryotherapy in FEVR-RRD with stage 3A or 4A FEVR and grade A or B PVR, especially in patients with multiple retinal holes.