Congenitally unguarded tricuspid valve orifice with a hypoplastic right ventricle and free thrombus in a giant right atrium

Patients with congenitally unguarded tricuspid valve orifice, along with associated abnormalities, rarely survive till adulthood. We report such a case, with a hypoplastic right ventricle and a floating thrombus in a giant right atrium, with intact interatrial and interventricular septa. The patient was managed surgically with satisfactory outcome.