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Hiroyuki Nakayasu
Hiroyuki Nakayasu
University of North Carolina at Chapel Hill
Biology
Sphingolipid
Molecular biology
Activator (genetics)
Schwann cell
5
Papers
335
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Ceramide accumulation is associated with increased apoptotic cell death in cultured fibroblasts of sphingolipid activator protein-deficient mouse but not in fibroblasts of patients with Farber disease
1999
Journal of Inherited Metabolic Disease
Jun Tohyama
Yasushi Oya
Takanori Ezoe
Marie T. Vanier
Hiroyuki Nakayasu
Nobuya Fujita
Kinuko Suzuki
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Citations (33)
The Cytoplasmic Domain of the Large Myelin-Associated Glycoprotein Isoform Is Needed for Proper CNS But Not Peripheral Nervous System Myelination
1998
The Journal of Neuroscience
Nobuya Fujita
April Kemper
Jeffrey L. Dupree
Hiroyuki Nakayasu
Udo Bartsch
Melitta Schachner
Nobuyo Maeda
Kinuko Suzuki
Kunihiko Suzuki
Brian Popko
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Citations (76)
Pathological study of mice with total deficiency of sphingolipid activator proteins (SAP knockout mice)
1998
Acta Neuropathologica
Yasushi Oya
Hiroyuki Nakayasu
Nobuya Fujita
Kunihiko Suzuki
Kinuko Suzuki
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Citations (37)
Targeted Disruption of the Mouse Sphingolipid Activator Protein Gene: A Complex Phenotype, Including Severe Leukodystrophy and Wide-Spread Storage of Multiple Sphingolipids
1996
Human Molecular Genetics
Nobuya Fujita
Kinuko Suzuki
Marie T. Vanier
Brian Popko
Nobuyo Maeda
Andreas Klein
Margarete Henseler
Konrad Sandhoff
Hiroyuki Nakayasu
Kunihiko Suzuki
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Citations (189)
SPHINGOLIPID ACTIVATOR PROTEIN "KNOCKOUT" MOUSE
1995
Nobuya Fujita
Kinuko Suzuki
T Vanier Marie
Brian Popko
Nobuyo Maeda
Hiroyuki Nakayasu
Kunihiko Suzuki
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