Familial internal carotid dissection

: Cervicocerebral arterial dissections is responsible for 20% of first strokes in young adults. Several diseases of the connective tissue and wall vessels anomalies are considered predisposing of arterial dissection. Familiar cases have been reported in 5%, according to hereditary primary arteriopathy, such as fibromuscular dysplasia. However, the nature of this arteriopathy has been rarely proved. We present two sisters with spontaneous dissection of the internal carotid artery with details suggestive of an atypical way of fibromuscular dysplasia in one of them.