Hypoplasia of the internal carotid artery associated with cerebral pseudoangiomatosis. Report of 4 cases.

Four cases of a peculiar cerebral vascular abnormality, consisting of hypoplasia and stenosis of the internal carotid artery, often bilateral, and of an unusual pseudoangiomatous cerebral circulation, are reported.Such a condition, originally found in Japanese patients only, has an undetermined cause.The information obtained through clinical and angiographic studies in these 4 cases seems to favor the hypothesis of a congenital and malformative origin of this vascular abnormality.