A Rare Case of Bilateral Inflammatory Linear Verrucous Epidermal Nevus

ABSTRACT Inflammatory linear verrucous epidermal nevus (ILVEN) is a rare, mosaicism-induced linear inflammatory dermatoses with early childhood presentation and persistence for whole life in majority of cases. No definite gene or genetic locus has been nominated yet. Treatment is mostly aimed for relief of symptoms and for cosmetic concerns. Here, authors are reporting a case of 6-year-old girl presented with history of extremely pruritic, erythematous, linear plaques following the lines of Blaschko over all 4 limbs, trunk and flexures since infancy. Clinical impression of bilateral ILVEN was confirmed by histopathology. No systemic abnormality was detected. Bilateral ILVEN is extremely rare entity and it should be documented whenever encounter.