Contemporary Early Postoperative Cone Repair Outcomes For Patients With Ebstein Anomaly

Introduction: Ebstein anomaly (EA) is a rare congenital heart defect characterized by abnormalities of the tricuspid valve (TV) leaflets and right ventricular (RV) cardiomyopathy. The current treatment for most patients with EA is cone reconstruction (CR) surgery. However, timing of repair has been highly variable, ranging from infancy to adulthood. Historically, surgical intervention for EA in the presence of severe RV failure has been associated with a longer intensive care unit course, increased need for ECMO support and a longer duration of mechanical ventilation. We sought to evaluate contemporary early postoperative outcomes in all age groups of patients with Ebstein …