The Importance Of Renal Angiomyolipoma In The Differential Diagnosis Of The Tuberous Sclerosis

SUMMARY Renal angiomyolipoma is a benign tumour containing adipose tissue, muscular tissue and vascular structures in different ratios. It consists of 3% of the kidney masses and is rarely seen in childhood. Renal angiomyolipoma is usually asymptomatic and detected incidentally. However, it may be a part of tuberous sclerosis complex disease and is seen in 50-75% of these patients. Thus, tuberous sclerosis complex disease should be excluded in cases with renal angiomyolipoma. We present two cases with renal angiomyolipoma detected incidentally upon evaluation for obesity and nonspecific abdominal pain. Although evaluation for tuberous sclerosis complex disease were negative at the moment, they are being followed up with respect to the development of other criteria for tuberous sclerosis complex disease.