Tumor infrecuente de pared torácica

2013 
Introduccion: el elastofibroma subescapular es un tumor relativamente raro de tejidos blandos. Se trata de una lesion no encapsulada y con contenido variable de colageno, grasa y fibras elasticas. Su incidencia es variable e infrecuente. En general, es infradiagnosticado y tiene un impacto incierto, dado que debe realizarse diagnostico diferencial con tumores subcutaneos como lipomas, fibrolipomas, formaciones quisticas o tumores mas agresivos. Objetivo: poner de manifiesto la importancia del diagnostico de estos tumores y su reseccion. Material y metodo: revision de la bibliografia y de historias clinicas de pacientes operados de tumores de dorso. Resultados: en el periodo enero 2011-marzo 2012 se evaluaron 4 pacientes que consultaron por tumores en region subescapular; 3 hombres y una mujer, con una edad media de 53 anos (rango, 45-64). En 3 de los casos, no tenian bilateralidad. Se estudiaron mediante exploracion fisica, junto a la ecografia y TAC toracica, con presencia de lesion subescapular sin invasion costal o pulmonar. En todos los casos, las intervenciones se realizaron con anestesia general y se efectuo la reseccion completa. Los pacientes fueron dados de alta entre el 1ro y el 2do dia del posoperatorio. No se registro mortalidad ni morbilidad. El diagnostico anatomopatologico fue elastofibroma de dorso en 3 de los casos y sarcoma en el caso restante. Conclusiones: si bien se lo considera un tumor infrecuente, generalmente esto se debe a que es una patologia infradiagnosticada. Se debe realizar diagnostico diferencias con neoplasias mesenquimales tipo liposarcomas, fibrosarcomas, histiocitoma fibroso maligno o metastasis. Es por eso que el tratamiento debe ser quirurgico dado que el diagnostico definitivo se realiza solo con la exeresis completa de la tumoracion y la malignidad no puede descartarse a menos que sea extirpado. Introduction: The subscapular elastofibroma is a relatively rare soft-tissue tumor. It is a non-encapsulated injury with variable content of collagen, fat and elastic fibers. It has a variable and infrequent incidence. Generally, it is underdiagnosed and has an uncertain impact since differential diagnosis must be made with subcutaneous tumors such as lipomas, fibrolipomas, cystic formations or more aggressive tumors.Objective: To show the importance of diagnosing these tumors and of their resection. Material and methods: Revision of references and the medical records of patients operated of dorsi tumors. Results: Between January 2011 and March 2012, 4 patients who consulted due to tumors in the subscapular region were assessed; they were 3 men and a woman, with an average age of 53 years old (range 45-64). In 3 of the cases, there were no symptoms; only one patient declared having suffered pain. One case presented bilaterality. The patients were studied by means of physical examination, together with the ultrasound and thoracic CT scans, showing subscapular injury without costal or lung invasion. In all cases, the patients were operated with general anesthesia and complete resection was carried out. Patients were released between the 1st and 2nd day of the postoperative period. Neither mortality nor morbidity were registered. The anatomopathological analysis provided 3 cases of elastofibroma dorsi and 1 case of sarcoma.Conclusions: Although it is considered an infrequent tumor, generally, that is due to the fact that it is an underdiagnosed pathology. Differential diagnosis must be made with mesenchymal neoplasms of the type of liposarcoma, malign fibrous histiocytoma or metastasis; therefore, treatment must be surgical since the definitive diagnosis is made only with the complete extirpation of the tumor and malignity cannot be ruled out unless the extirpation has been performed.
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