Dural Fistula: A Rare Cause of Diffuse Intracerebral Calcification

Introduction: Fahr syndrome is typically diagnosed in younger individuals when secondary causes like endocrine, infections, vasculitis, vascular malformation, radiation, chemotherapy, carbon monoxide poisoning, mitochondrial myopathy are identified with appropriate intracranial imaging featuresCase Presentation: We describe the neuroimaging findings in a 16-year-old male presented with headache, vomiting and seizure with anomalous intracranial venous drainage and cerebral calcification. Computed Tomography (CT) scans demonstrated that his diffuse cerebral calcification involving basal ganglia and also subcortical white matter of fronto-parietal lobe, where Magnetic Resonance Imaging (MRI) Brain showed chronic infarct in right cerebellar hemisphere with marginal gliosis. Magnetic resonance angiography of Brain showed fistulous connection with sigmoid sinus. Magnetic resonance venography of brain dilated cortical vein with cerebral venous sinuses without thrombus in situ.Conclusion: The possible relationship between cerebral calcification and anomalous intracranial venous drainage has been discussed.