[Bessef Hogen's disease, or exostosis disease, with spinal cord compression: a case in the service of the Paediatric CHU Ouedraogo, Ouagadougou, BF].

: CA, 14 old years, female, born last uterine siblings of 9 children, 4 died of various causes, was admitted in the pediatric service of CHU-YO for functional impairment of the lower limbs. Physical examination revealed swelling and deformation harsh, uneven surfaces, the circumferential upper and lower limbs and lumbar spine associated with spastic paraplegia. Sphincter disturbances accompany this clinical picture. The radiographic bone marrow hypertrophy individually with images of exostosis at the epiphyses. Multiple exostosis or BESSEF Hogen's disease is rare and has a reserve functional prognosis because of outcome of low spinal cord compression and vascular compression. We felt it appropriate to bring this case discovered during our clinical practice because of its rarity and the risk of malignant degeneration. : La radiographie osseuse individualise une hypertrophie osseuse avec des images d'exostose au niveau des epiphyses. : Affection rare, l'exostose ou maladie des exostoses multiples de BESSEF HOGEN a un pronostic fonctionnel reserve du fait des compressions medullaires basses et vasculaires. Nous avons juge opportun de rapporter ce cas decouvert lors de notre pratique clinique a cause de sa rarete et du risque de degenerescence maligne.