18F-FDG PET/CT in a patient with atypical presentation of cardiac angiosarcoma

Abstract Primary cardiac or pericardial tumors are infrequent, metastatic involvement being more common. Cardiac angiosarcoma is a rare primary malignant tumor of mesenchymal origin. It entails a poor prognosis mostly due to frequent metastases at the time of diagnosis, as well as low response to onco-specific treatments. We describe a case of a 74-year-old patient with a primary cardiac angiosarcoma with an infrequent location at pericardium level. We review the literature and the utility of 18 F-FDG PET/CT in the initial staging.