Epithelioid Sarcoma of the Vulva

Vulval epithelioid sarcoma is a rare, locally-aggressive malignant soft tissue tumour, which may present diagnostic diffi culties, both clinically and pathologically. This can result in a delay in appropriate treatment, which consists primarily of radical wide local excision of the tumour. We report a case of a recurrent epithelioid sarcoma of the vulva, with a discussion of the pathological features and management.