Keratitis, ichthyosis and deafness (KID syndrome).

Summary A boy with ichthyosiform erythroderma also suffered from sensorineural deafness, superficial punctate keratitis and acanthosis nigricans. Histopathology revealed basket weave hyperkeratosis, hydropic degeneration of the basal layer, melanin incontinence and moderate mononuclear infiltrate. Typical histological changes were found in clinical lesions of acanthosis nigricans.