Radiological feature of skip-segment Hirschsprung’s disease

A term neonate was hospitalised for progressive abdominal distension and delayed meconium passage on his third day of birth. Plain abdominal radiograph revealed no gas in the distal colon. Constrast enema study revealed narrow rectosigmoid and descending colon with a transitional zone at the left transverse colon (figure 1). Rectal biopsy was performed, which showed an absence of ganglion cells in the lamina propria. Diagnosed with long-segment Hirschsprung disease (HD), the patient was managed with rectal irrigations at home. At the age of 3 months, he underwent laparoscopic transanal pull-through procedure. At laparoscopy, the distal colon was collapsed with a classic …