Persistent Mullerian Duct Syndrome - A Rare Anomaly

Persistent mullerian duct syndrome is a disorder of male pseudo-hermophraditism characterized by persistence of uterus, fallopian tubes and upper two third of vagina in otherwise normally virilized phenotypically and genotypically male (46XY). Patients may present with hernia, hydrocele, or impalpable udescended testis at any age group and most of them are diagnosed intraoperatively. Awareness among the surgeons about this rare association helps in appropriate management.