Congenital Malignant Rhabdoid Tumor of the Skin-Report of a Case and Review of the Literature

Malignant rhabdoid tumor is a well-established clinicopathologic entity occurring classically in the kidney and central nervous system in children. Cutaneous origin has rarely been reported. We herein report a male newborn infant presented with an erythematous and ulcerated mass on his lower back at birth and was found to be a malignant rhabdoid tumor, diagnosed by histopathologic and immunohistochemical studies. In spite of aggressive treatment with chemotherapy and surgery, cerebral and pulmonary metastases developed later. The patient finally died at 10 months of age. This rare case is reported and literatures are reviewed.