Prune Belly Syndrome

Prune belly syndrome, also referred to as Eagle-Barrett syndrome or the triad syndrome, is a rare congenital disorder characterized by the triad of deficient abdominal musculature, cryptorchidism, and urinary tract abnormalities. Children born with this condition present on a broad spectrum ranging from incompatibility with life to aging normally and having children of their own. The severity of renal dysplasia mostly determines the survival and prognosis among the survivors. Perinatal mortality ranges between 10 to 25% in contemporary studies and directly correlates to the severity of pulmonary hypoplasia as a result of oligohydramnios from reduced fetal urine production from renal dysplasia and urinary tract abnormalities leading to Potter sequence.