Left ventricular restoration surgery for isolated left ventricular noncompaction: report of the first successful case.

Left ventricular (LV) noncompaction (LVNC) is a rare congenital dysfunction of ventricular morphogenesis resulting from arrested muscle fiber compaction in early embryogenesis. We report a first successful case of left ventricular restoration (LVR) surgery in a patient with LVNC with severe LV dysfunction. LVR of septal anterior ventricular exclusion and concomitant mitral and tricuspid annuloplasty were successfully performed.