Papillon-Lefèvre Syndrome - A Case Report and a Multidisciplinary approach in the Treatment of 18 Years Old Sudanese Female

An eighteen years old Sudanese female patient presented with keratotic plaques over the skin of her palms and soles and swollen gums since the age of 4 years with the subsequent loss of most of her primary and permanent dentition. These findings are consistent with Papillon-Lefevre syndrome. Papillon-Lefevre syndrome is a rare autosomal recessive genetic disorder with a clinical presentation which includes palmer planter keratoderma associated with the precocious progressive periodontal disease that results in early exfoliation of both the primary and permanent dentitions.