Perivascular epithelioid cell tumor (PEComa) presents an endometrial polyp pattern: Case report and literature review

Abstract Perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal tumor composed of histologically and immunohistochemically distinctive perivascular epithelioid cells [ 1 , 2], which can arise in a wide array of anatomic locations, and is characterized by its myelomelanocytic phenotype and unpredictable natural history. To date, less than 80 cases of uterine PEComa have been reported in the literature [3]. Although almost all of these cases show a mural or subserosal localization. Here, we report a rare pattern of uterine PEComa which present as polypoid lesions mimicking an endometrial polyp in a 47-year-old Chinese woman.