Churg-Strauss syndrome in a child: retina and optic nerve findings

Allergic granulomatosis and angiitis, also known as Churg-Strauss syndrome (CSS) is predominantly a disease of adults.1 Ocular involvement is rare.2 We describe a case of CSS in a child that resulted in bilateral optic neuropathy with vasculitis and multiple branch retinal artery occlusions affecting the macula. A 10 year old African-American girl developed sudden painless loss of vision in both eyes over 2 days. The child was an inpatient admitted for examination of a multisystem disorder, affecting her pulmonary, gastrointestinal, muscular, and renal systems. On examination the best corrected vision was hand movement in both eyes. Confrontation visual fields were full bilaterally. Pupils were normal, without an afferent papillary defect. Anterior segment examination was completely …