ELEVATED PHENYLACETIC ACID LEVELS DO NOT CORRELATE WITH ADVERSE EVENTS IN PATIENTS WITH UREA CYCLE DISORDERS OR HEPATIC ENCEPHALOPATHY AND CAN BE PREDICTED BASED ON THE PLASMA PAA TO PAGN RATIO

Elevated phenylacetic acid levels do not correlate with adverse events in patients with urea cycle disorders or hepatic encephalopathy and can be predicted based on the plasma PAA to PAGN ratio☆ M. Mokhtarani ⁎, G.A. Diaz , W. Rhead , S.A. Berry , U. Lichter-Konecki , A. Feigenbaum , A. Schulze , N. Longo , J. Bartley , W. Berquist , R. Gallagher , W. Smith , S.E. McCandless , C. Harding , D.C. Rockey , J.M. Vierling , P. Mantry , M. Ghabril , R.S. Brown Jr. , K. Dickinson , T. Moors , C. Norris , D. Coakley , D.A. Milikien , S.C. Nagamani , C. LeMons , B. Lee , B.F. Scharschmidt a