Síndrome de Mayer-von Rokitansky-Küster-Hauser

Introduction: The Mayer-von Rokitansky-Kuster-Hauser (MRKH) syndrome happens in approximately one of 5000 women born alive and is the commonest cause of congenital absence of the vagina. Method: We present two cases handled surgically by means of abdomino-perineal correction with intestine interposition, performed by the specialties of Pediatric Gynecology and Coloproctology in the Hospital San Ignacio. Given the clinical and paraclinical findings, the creation of a neovagina it was considered the best therapeutic option for our patients, using a segment of sigmoid colon, since these patients did not have any degree of vaginal tube that could be dilatable. Conclusions: The surgical approach in vaginal agenesis is one of the best types of treatments which we have to offer to these patients, among these the sigmoid neovagina is a technique with excellent results and relatively few complications, which has demonstrated to be adequately accepted by patients.