Congenital cholesteatoma of the middle ear in a child with aural atresia complicated by mastoid abscess

: Authors have described the case of infected congenital cholesteatoma of the middle ear with congenital atresia of external auditory canal in a 12-year-old child. Congenital aural cholesteatoma was not recognized for aural atresia of external canal and middle ear space. Then mastoid abscess appeared due to infection that arose from nasopharyngs through Eustachian tube to middle ear space. Intraoperatively behind atretic canal closed by atretic plate, in the middle ear space cholesteatoma was found. Surgery for this patient consisted of removing cholesteatoma, canaloplasty and ossiculoplasty. Despite the destruction caused by cholesteatoma and surgical intervention excellent functional results that means hearing improvement were obtained.