LOW-GRADE FIBROMYXOID SARCOMA OF THE MAXILLA. REPORT OF A CASE

Low-grade fibromyxoid sarcoma (LGFS) is a variant of fibrosarcoma that commonly arises in the deep soft tissues of the lower extremities in young or middle-aged adults. It is characterized by high rates of local recurrence and late metastases, despite its deceptively benign image. We report the case of a 45-year-old man referred for a swelling of his left maxilla for 15 years’ duration. An incisional biopsy showed a proliferation of bland spindle and stellate-shaped cells, deposited in an alternating myxoid and fibrous stroma. Diagnosis of odontogenic myxoma and LGFS were proposed. A computed tomography showed an expansive and well-defined tumor in the left maxillary sinus and maxilla, without regional lymph node involvement or metastases. A complete resection of the tumor was performed and the diagnosis of LGFS was confirmed. Adjuvant treatment was not required and after 1 year follow-up, the patient remains free of disease.