AB031. Management of congenital cystic adenomatoid malformation in newborns.

Congenital cystic adenomatoid malformations (CCAM), also known as congenital pulmonary airway malformation, is a developmental defect of the respiratory tract, with unknown etiology. It is a rare disease, with an incidence of 1 in 8,300 to 1 in 35,000 but also the most common congenital lung anomaly. We present a newborn boy, GA 31+6 weeks, who was diagnosed with left CCAM at GA 20+ weeks. We did echo-guide pig-tail insertion for decompression soon after delivery, and we arranged posterolateral thoracotomy left lower lobe lobectomy 4 days later when vital sign stabilized. His post-operative course was smooth and final pathology report showed type II CCAM.