Case Report モヤモヤ病と診断4 年後に全身性エリテマトーデスを発症した1 例

A 7-year-old female presented with syncope attack when she cried and the symptoms gradually deteriorated.She consulted our hospital in 2001. Magnetic Resonance Imaging (MRI) demonstrated cerebral infarctions atthe bilateral frontal lobes. Digital subtraction angiography (DSA) revealed Moyamoya disease stage ㈽.Bilateral encephaloduroarteriosynangiosis (EDAS) was performed. The postoperative course was good and thesymptoms disappeared. In May 2005, she felt general fatigue and was diagnosed with systemic lupus erythematosus(SLE) based on a typical malar rash, a positive antinuclear antibody, and high titer anti-double-strandDNA. She was treated with systemic steroid administration.Key Words: moyamoya disease, SLE, EDAS