901 ACQUIRED VON WILLEBRAND'S DISEASE (vWD) SECONDARY TO SPLENIC HEMANGIOMA

Acquired vWD was found in a 24 yr. old girl who presented with ecchymoses and conjunctival hemorrhages. Marked splenomegaly was present. Diffuse hemangiomatous transformation of the spleen suspected clinically, by CT scan and antiography, was confirmed at surgery. Coagulation studies were done at diagnosis, pre- and post-DDAVP infusion (0.3 mcg/kg) and 1 week post-splenectomy.