Dermatofibrosarcoma protuberans in atypical inguinal location: Diagnosis, treatment and follow-up scheme.

OBJECTIVE To review dermatofibrosarcoma protuberans (DFSP), which is a soft tissue neoplasm of the skin that can rarely affect the genitals. MATERIAL AND METHOD We report a case of inguinal DFSP in a 40-year-old male who presented a slow-growing mass adjacent to the spermatic cord. RESULTS After extensive surgical resection pathological analysis confirmed the diagnosis of DFSP with resection margins affected, so reoperation with margin exeresis and inguinal orchiectomy was required. CONCLUSIONS DFSP is rarely localized in the inguinoescrotal region and it requires wide excision and sometimes orchiectomy.