Budd-Chairi syndrome with intussusception a unique and rare presentation of celiac disease

The association of Budd-Chiari syndrome (BCS) and celiac disease is rare, reported in only 15 cases. None of the case of Budd- Chiari with transient intussusception in celiac disease (in same patient) reported in literature till now. We, hereby, report a 5-year-old male, known case of celiac disease, who presented with pain and distention of abdomen, and failure to thrive for last 2 years. The child had hepatomegaly with fluid thrill. Ultrasonography abdomen showed caudate lobe hypertrophy, transient intussusception with dilated vascular channel and on contrast enhanced computed tomography scan; features suggestive of BCS were found.