Extranodal Rosai–Dorfman disease as a pelvic mass

.  Leiva BJL, Bofill RM, Sevin B-U, Geiger XJ. Extranodal Rosai–Dorfman disease as a pelvic mass. Int J Gynecol Cancer 2006;16(Suppl. 1):312–315. Rosai–Dorfman disease (RDD) is a rare histiocytic disorder of unknown cause. RDD most commonly involves the cervical lymph nodes, but extranodal involvement has been described. We report the case of a patient with extranodal RDD that presented as a retroperitoneal mass obstructing the left ureter. The patient underwent surgical resection of the mass, followed by a 5-month course of vinblastine. There was no evidence of progressive disease 22 months after surgery.