Neurofibromatosis presenting as painless clitoromegaly.

Received June 2008 Accepted September 2008 INTRODUCTION Neurofibromatosis is an autosomal dominant progressive disorder with an incidence of approximately 1 in 3000 live births.(1) Its recognized features include hyperpigmented skin lesions (cafe-au-lait spots), neurofibromas, iris hamartomas, macrocephaly, central nervous system tumors, defects of the skull and facial bones, and vascular lesions. Involvement of the external genitalia is extremely unusual.(1,2) We present a case of a neurofibroma of the dorsal clitoral hood and its management.