SECONDARY PULMONARY ARTERIAL HYPERTENSION IN A PATIENT WITH COMMON VARIABLE IMMUNODEFICIENCY: TREATMENT WİTH LOW DOSE SILDENAFIL

The present report describes a patient with common variable immunodeficiency who suffered severe pulmonary arterial hypertension and bilateral lung destruction due to bronchiectasis. Initially, the patient's treatment included antibiotics, diuretics, bronchodilators, mucolytics, oxygen and immunoglobulin replacement therapy. However, the patient's condition improved significantly only after low dose sildenafil treatment. To our best notice, our patient is the first report displaying a favorable outcome with sildenafil treatment in secondary pulmonary hypertension.