Simultaneous Repair of Right-Sided Coarctation and Vascular Ring

We present the case of a 4-year old girl with posterior fossa–hemangioma–arterial lesions–cardiac abnormalities/coarctation–eye abnormalities (PHACE) syndrome, an atypical, long-segment, right-sided coarctation of the aorta and vascular ring secondary to an aberrant left subclavian artery and left ligamentum. Simultaneous repair of both lesions was accomplished using a novel technique that included reimplantation of the aberrant left subclavian artery and translocation of the descending aorta to the proximal ascending aorta.