Rhabdomyosarcoma arising within the biliary tract mimicking a choledochal cyst: A case report

Rhabdomyosarcoma (RMS) involving the biliary tree and choledochal cysts presents with jaundice and abdominal pain. Imaging studies including ultrasound (US), computerized tomography (CT) scan, and magnetic resonance cholangiopancreatography (MRCP) are useful in the diagnosis and evaluation of biliary tree anatomy. We present a patient with biliary RMS initially thought to be a choledochal cyst with intraluminal cystic debris (biliary sludge) that was diagnosed by frozen section examination during cyst resection and subsequently treated with post-operative chemotherapy and radiation.