Surgical treatment for epilepsy due to Sturge-Weber syndrome:a case report and review of the literature

Objective To explore the strategy and its effect of surgical treatment of epilepsy and development retardation due to Sturge-Weber syndrome.Methods The clinical data of an infant surgically treated for epilepsy,mental and physical development retardation due to Sturge-Weber syndrome were retrospectively reviewed.After sufficient preoperative evaluation,the operation was performed through the hemisphere craniectomy,and the right total parietal lobe,partial frontal temporal and occipital lobes were removed.Results The muscle force of left limbs was grade I post operation,but they recovered gradually after 3 days,and recovered to preoperative level after 3 weeks.During the 18 months interval of follow-up the patient was seizure free,her muscle force of right upper limb improved to grade V-,left fingers movement improved significantly,aggressive behaviour disappeared,and DQ improved from preoperative 48 to 75.Conclusion Epilepsy and development retardation due to Sturge-Weber syndrome can be treated by resection the cortex of involved multiple brain lobes. Key words: Sturge-Weber Syndrome;  Epilepsy;  Neurosurgical procedures