A treatment case of a pachydermatocele with von Recklinghausen's disease in the mid-face and oral cavity

Report of a 29-year old female with von Recklinghausen's disease by the presence of pachydermatocele, multiple cafe-au-lait spot and benign neurofibroma.The tumor, which hung down to an upper eyelid, the cheek, the nose, and oral cavity on the right side, existed and the lower eyelid was swollen upwards.(pachydermatocele)1. Resection of tumor:We made excisions on the intra-oral and mid-facial tumor. Histopathologicaly, both of them, were Neurofibroma.2. Reconstruction:The lacking of skin part was formed again by using D-P flap.3. Plastic surgery:The form of the eyelid was corrected by Mustarde flap. Lower eyelid and transplant were raised with iliotibial tract. The facial configuration, which was able to be satisfied mostly with the above-mentioned operation, was obtained. Prosthodontic treatment was given to the toothless area and the occlusal function has been improved.The tumor does not recrudescence, and the passage is excellent now.