Nutrition in Dystrophic Epidermolysis Bullosa

: In dystrophic epidermolysis bultosa (EB), a combination of diminished food intake and Increased nutritional requirements commonly leads to mainourishment Adequate nutrition in these patterns could pro-vide many benefits, including Improved growth, accelerated healing, de-creased susceptibility to infection, and enhanced well-being. We as-sessed nutrition status of children with dystrophic EB, and evaluated the benefits of nutritional advice in those who were considered malnour-ished. The majority of patients had inadequate Intakes of a wide spectrum of nutrients, Including those who appeared to be relatively mildly af-fected. We were unable to secure persisting substantial Improvements In dietary intake despite thorough counseling. Adequate nutrition In pa-tients with dystrophic EB depends on active nutritional support starting from birth. The need for more invasive techniques of nourishment, such as nasogastric and gastrostomy feeding, may have to be considered earlier than Is currently the case.