Acquired Chiari I malformation secondary to generalized hyperostotic skull: a case report and literature review

Objective Acquired Chiari Ⅰ malformation associated with generalized hyperostotic skull is a rare condition.The management of this condition is far more different from congenital and other kind of acquired Chiari Ⅰ malformation.This study tried to establish an individual management plan for these patients.Method A 22 - year old female patient was admitted for headache and papilledema.Generalized hyperostotic skull and secondary Chiari Ⅰ malformation were found after examination.This case was reported and related literatures were reviewed.Results Most cases of generalized hyperostosis of skull are associated with Camurati - Engelmann disease,craniodiaphyseal dysplasia,Worth - type endosteal hyperostosis,sclerosteosis,or other conditions.Infrequently,a Chiari malformation may also be described.This patient was a Worth - type endosteal hyperostosis and the surgical approach of subtemporal decompression was taken.Conclusions Acquired Chiari Ⅰ malformation is rarely associated with hyperostosis of skull.For a patient with symptom,a procedure of subtemporal decompression should be taken and suboccipital approach should be prohibitive. Key words: Acquired Chiari malformation;  Hyperostosis;  Subtemporal decommpression