Ectodermale dysplasie : een heterogene afwijking

: The 'problem' of ectodermal dysplasia is discussed in conjunction with a case report and a review of the literature. In a range of hereditary disorders all ectodermal structures can be effected in a variable way: reduction of the amount of hair, sweat glands and sebaceous glands, and a complete or partial anodontia of the deciduous and permanent dentition with malformation of the erupted teeth.