Aggressive Angiomyxoma Clinical Images

Aggressive angiomyxoma (AAM) is a rare, commonly infiltrative mesenchymal tumor presenting mainly in the inguinal and perineal region of reproductive-age females, between the second and fourth decades of life, with vague symptoms. Surgical resection is the treatment. We describe a case of a perineal aggressive angiomyxoma in a 44-year-old woman in which the diagnosis was made after histological examination. Close long-term follow-up by MRI is mandatory. Most recurrences are local, within the first 3 post-operative years. There are no reports of AAM as cause of death, although multiple-recurrence cases can impact quality of life.