scleroderma - Pulmonary manifestations
2015
Scleroderma is a chronic disease of unknown etiology, usually classified with the collagen diseases. The term diffuse or progressive systemic sclerosis has been introduced to describe those cases showing visceral as well as cutaneous manifestations. The essential pathological features are swelling and disintegration of the collagen tissue accompanied by cellular infiltration and fibrosis; the process may also involve the intima of small vessels with fibrinoid necrosis and occlusion. In this article we would like to present two cases of systemic sclerosis. Case 1: A 30 year old lady showed early changes suggestive of systemic sclerosis along with marked skin changes. Her ANA profile supported Diffuse systemic sclerosis .Case 2:A 64 year old female complaining of severe dyspnoea presented with marked skin changes which were pathognomic of scleroderma .On evaluation findings supported diffuse systemic sclerosis and radiologically showed late changes in respiratory system. We intend to report these two cases to show two different ends in the spectrum of presentation of pulmonary manifestations of systemic sclerosis. Case 1 had less symptomatology compared to Case 2.
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