Solitary fibrous renal tumor with thrombus extension into the inferior vena cava and right atrium

A solitary fibrous tumor of the kidney with thrombus extended into the inferior vena cava and right atrium is very rare. The current surgical approach is to combine intra-abdominal and cardiac surgery with cardiopulmonary bypass. We describe a rare case of renal solitary fibrous tumor extended to the inferior vena cava and right atrium, treated with urgent cardiac surgery using deep hypothermic circulatory arrest one month after an inappropriate right nephrectomy because of the development of cavo-atrial obstruction symptoms.