PERAWATAN GIGI PADA ANAK DENGAN MAPLE SYRUP URINE DISEASE (LAPORAN KASUS)

Maple Syrup Urine Disease is a disparity of leusin decarboxilation, and isoleusin of valin defect that is synthesized with complex enzyme systems. It is a rare disease and represents disparity. In some cases can generate ketosis that grows according to health change and can cause comma. Dental treatment of a child with  Maple Syrup Urine Disease was not clearly mentioned, there is only a factor such as infection, which is very dangerous at any age, and can generate irregular metabolism. Dental treatment of a child with  Maple Syrup Urine Disease accompanied by mental retardation must be done continuously to avoid infection that can result in the death of the patients.