Nefroma mesoblástico congénito. Aspectos genéticos y tomográficos

Introduction. Congenital mesoblastic nephroma (CMN) is a benign solid renal tumor; CMN is infrequent although it is the commonest renal tumor observed in infants. CMN is composed of interlacing bundles of spindle-shaped cells with low nuclear atypia and mitotic activity; it does not usually metastatize, and surgical resection is curative. Case report. A full term male presented at birth with a palpable mass in the right abdomen; the rest of the clinical examination was normal. A large, well defined tumor, without calcifications was observed in an abdominal radiography. A non-homogeneous tumor, with well delineated borders, arising from the right kidney was disclosed on CT scan examination. The tumor was surgically resected and the patient is doing well 2 years after discharge. Conclusion. CMN represent 80% of solid renal masses in neonates, it is usually discover just after birth as an abdominal mass; is more common than Wilms 1 tumor in infant under 30 months of age. It differs from Wilms' tumor in its earlier presentation, histological features, and its favorable prognosis as observed in our case.