Atipik Dyke-Davidoff-Masson Sendromlu bir Olgu

Dyke-Davidoff-Masson syndrome (DDMS) is a rare occurrence characterized by epileptic seizures, facial asymmetry or hemiparesis, mental retardation, sensory neural hearing loss, cerebral hemiatrophy in radiologic imaging, single sided thickness of the head along with increase in paranasal sinus and petrous bone ventilation. Congenital pathologies, prenatal diseases, birth trauma, brain masses, febrile seizures and brain vein diseases are held responsible in its etiology. Twenty four year old female patient applied to the emergency clinic with complaints of seizures that occurred twice in the past 1 month starting on the right side of the face and arm then spreading out to all the body coupled with blockout. She had a history of falling from a height when she was 5 years old. Physical examination was normal. In the cranial magnetic resonance imaging, there was a slight widening in the left lateral ventricule, volume decrease and ensephalomalacia in the left temporopariatel lobe. The patient was admitted to neurology clinic and her electroencephalography (EEG) was normal. No mental retardation was observed in the WISC-R test. We presented a case observed rarely in advanced age with radiological DDMS diagnosis having no symptom other than clinical seizures