Cordoma cervical paravertebral, entidad que debemos conocer: A propósito de un caso

espanolEl cordoma es un tumor raro de lento crecimiento, derivado de remanentes de la notocorda. La mayoria se localizan en la base del craneo y en la region sacrococcigea, mostrando una localizacion cervical en solo el 6% de los casos. Presentamos el caso, poco frecuente (se han reportado menos de 10 en la literatura), de un cordoma paravertebral izquierdo, localizado a nivel de C2-C4, en un varon joven sin antecedentes personales de interes. Los hallazgos radiologicos sugerian que se trataba de una neoplasia de crecimiento lento, de predominio quistico, que erosionaba estructuras oseas y englobaba a la arteria vertebral izquierda. Se planifico exeresis quirurgica y en el analisis de la pieza se observo proliferacion celular con estroma de aspecto mixo-condroide, celulas epitelioides y fisaliferas (PAS+), todo ello compatible con cordoma. EnglishChordoma is a rare, slow-growing tumour arising from remnants of the notochord. It is most often located in the base of the skull and the sacrococcygeal region, being located in the cervical region in only 6% of cases. A rare case is presented of a left para-spinal chordoma, of which less than 10 cases have been reported in literature. It was located at C2-C4 level in a young male with no personal history of interest. Radiographic findings suggested that this was a slow-growing tumour, of cystic dominance, which eroded the bone structures and encompassed the left vertebral artery. Surgical excision was performed, and in the analysis of the surgical piece, cell proliferation was observed, with a stromal myxoid-chondroid appearance, epithelioid and physaliphorous (PAS+) cells, all of them compatible with chordoma.