Benign lipoblastoma of the upper limb: a case report and literature review

2014 
Lipoblastoma is a rare mesenchymal tumor occurring primarily in pediatric patients and formed by lipoblasts that proliferate after the postnatal period. Despite its potential for local invasion and rapid growth, its prognosis is excellent. In this study, we report the case of a pediatric patient with a ponderous lesion in the right forearm that caused considerable functional impairment of the affected limb. We also discuss the relevant aspects concerning the differential diagnosis and management of the disease, as it has the potential to cause incapacity without proper treatment. O lipoblastoma e um tumor mesenquimal raro, composto de lipoblastos que continuam sua proliferacao apos o periodo pos-natal e que acometem, predominantemente, a populacao pediatrica. Apresenta prognostico excelente, apesar do potencial de invasao local e do crescimento rapido. Os autores relatam o caso de uma paciente pediatrica portadora de volumosa lesao em antebraco direito, ocasionando importante comprometimento funcional do membro acometido. Aspectos relevantes no diagnostico diferencial e manejo sao discutidos neste trabalho, visto tratar-se de lesao com potencial risco incapacitante futuro, caso nao manejada corretamente.
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