Sustitución valvular mitral en paciente con síndrome de Ehlers-Danlos

The presence of a mitral valve prolapse could be to an alteration in the type III type collagen formation with a myxomatous degeneration and accumulation of mucopolysaccharides in mitral valves and sometimes in the subvalvular tract being the more frequent cardiovascular expression of the Ehlers-Danlos syndrome. To describe the anesthetic-surgical behavior of a patient with severe mitral insufficiency provoked